ICD-10-CM > E00-E89 > E70-E88 > E75 > E75.2 E75.2 Other sphingolipidosis Non-Billable/Non-Specific Type 1 Excludes adrenoleukodystrophy [Addison-Schilder] (E71.528) Codes E75.21Fabry (-Anderson) diseaseE75.22Gaucher diseaseE75.23Krabbe diseaseE75.24Niemann-Pick diseaseE75.240Niemann-Pick disease type AE75.241Niemann-Pick disease type BE75.242Niemann-Pick disease type CE75.243Niemann-Pick disease type DE75.244Niemann-Pick disease type A/BE75.248Other Niemann-Pick diseaseE75.249Niemann-Pick disease, unspecifiedE75.25Metachromatic leukodystrophyE75.26Sulfatase deficiencyE75.27Pelizaeus-Merzbacher diseaseE75.28Canavan diseaseE75.29Other sphingolipidosis