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E70-E88 Metabolic disorders

Type 1 Excludes

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Type 2 Excludes

  • Ehlers-Danlos syndromes (Q79.6-)

Codes

  • E70Disorders of aromatic amino-acid metabolism
  • E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
  • E72Other disorders of amino-acid metabolism
  • E73Lactose intolerance
  • E74Other disorders of carbohydrate metabolism
  • E75Disorders of sphingolipid metabolism and other lipid storage disorders
  • E76Disorders of glycosaminoglycan metabolism
  • E77Disorders of glycoprotein metabolism
  • E78Disorders of lipoprotein metabolism and other lipidemias
  • E79Disorders of purine and pyrimidine metabolism
  • E80Disorders of porphyrin and bilirubin metabolism
  • E83Disorders of mineral metabolism
  • E84Cystic fibrosis
  • E85Amyloidosis
  • E86Volume depletion
  • E87Other disorders of fluid, electrolyte and acid-base balance
  • E88Other and unspecified metabolic disorders