ICD-10-CM > E00-E89 > E70-E88 > E75 > E75.2 > E75.24 > E75.244 E75.244 Niemann-Pick disease type A/B Billable/Specific Copy Code Copy Description Applicable To Acid sphingomyelinase deficiency type A/B (ASMD type A/B)Chronic neurovisceral acid sphingomyelinase deficiency