ICD-10-CM > E00-E89 > E70-E88 > E75 > E75.2 > E75.24 > E75.240 E75.240 Niemann-Pick disease type A Billable/Specific Copy Code Copy Description Applicable To Acid sphingomyelinase deficiency type A (ASMD type A)Infantile neurovisceral acid sphingomyelinase deficiency