ICD-10-CM > E00-E89 > E70-E88 > E75 > E75.2 > E75.24 > E75.241 E75.241 Niemann-Pick disease type B Billable/Specific Copy Code Copy Description Applicable To Acid sphingomyelinase deficiency type B (ASMD type B)Chronic visceral acid sphingomyelinase deficiency