ICD-10-CM > Q00-QA0 > Q80-Q89 > Q87 > Q87.4 Q87.4 Marfan syndrome Non-Billable/Non-Specific Codes Q87.40Marfan syndrome, unspecifiedQ87.41Marfan syndrome with cardiovascular manifestationsQ87.410Marfan syndrome with aortic dilationQ87.418Marfan syndrome with other cardiovascular manifestationsQ87.42Marfan syndrome with ocular manifestationsQ87.43Marfan syndrome with skeletal manifestation