ICD-10-CM > E00-E89 > E70-E88 > E74 E74 Other disorders of carbohydrate metabolism Non-Billable/Non-Specific Type 1 Excludes diabetes mellitus (E08-E13)hypoglycemia NOS (E16.2)increased secretion of glucagon (E16.3)mucopolysaccharidosis (E76.0-E76.3) Codes E74.0Glycogen storage diseaseE74.00Glycogen storage disease, unspecifiedE74.01von Gierke diseaseE74.02Pompe diseaseE74.03Cori diseaseE74.04McArdle diseaseE74.05Lysosome-associated membrane protein 2 [LAMP2] deficiencyE74.09Other glycogen storage diseaseE74.1Disorders of fructose metabolismE74.10Disorder of fructose metabolism, unspecifiedE74.11Essential fructosuriaE74.12Hereditary fructose intoleranceE74.19Other disorders of fructose metabolismE74.2Disorders of galactose metabolismE74.20Disorders of galactose metabolism, unspecifiedE74.21GalactosemiaE74.29Other disorders of galactose metabolismE74.3Other disorders of intestinal carbohydrate absorptionE74.31Sucrase-isomaltase deficiencyE74.39Other disorders of intestinal carbohydrate absorptionE74.4Disorders of pyruvate metabolism and gluconeogenesisE74.8Other specified disorders of carbohydrate metabolismE74.81Disorders of glucose transport, not elsewhere classifiedE74.810Glucose transporter protein type 1 deficiencyE74.818Other disorders of glucose transportE74.819Disorders of glucose transport, unspecifiedE74.82Disorders of citrate metabolismE74.820SLC13A5 Citrate Transporter DisorderE74.829Other disorders of citrate metabolismE74.89Other specified disorders of carbohydrate metabolismE74.9Disorder of carbohydrate metabolism, unspecified