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E78 Disorders of lipoprotein metabolism and other lipidemias

Non-Billable/Non-Specific

Type 1 Excludes

Codes

  • E78.0Pure hypercholesterolemia
    • E78.00Pure hypercholesterolemia, unspecified
    • E78.01Familial hypercholesterolemia
      • E78.010Homozygous familial hypercholesterolemia [HoFH]
      • E78.011Heterozygous familial hypercholesterolemia [HeFH]
      • E78.019Familial hypercholesterolemia, unspecified
  • E78.1Pure hyperglyceridemia
  • E78.2Mixed hyperlipidemia
  • E78.3Hyperchylomicronemia
  • E78.4Other hyperlipidemia
  • E78.5Hyperlipidemia, unspecified
  • E78.6Lipoprotein deficiency
  • E78.7Disorders of bile acid and cholesterol metabolism
    • E78.70Disorder of bile acid and cholesterol metabolism, unspecified
    • E78.71Barth syndrome
    • E78.72Smith-Lemli-Opitz syndrome
    • E78.79Other disorders of bile acid and cholesterol metabolism
  • E78.8Other disorders of lipoprotein metabolism
    • E78.81Lipoid dermatoarthritis
    • E78.89Other lipoprotein metabolism disorders
  • E78.9Disorder of lipoprotein metabolism, unspecified