ICD-10-CM > Q00-QA0 > Q80-Q89 > Q89 Q89 Other congenital malformations, not elsewhere classified Non-Billable/Non-Specific Codes Q89.0Congenital absence and malformations of spleenQ89.01Asplenia (congenital)Q89.09Congenital malformations of spleenQ89.1Congenital malformations of adrenal glandQ89.2Congenital malformations of other endocrine glandsQ89.3Situs inversusQ89.4Conjoined twinsQ89.7Multiple congenital malformations, not elsewhere classifiedQ89.8Other specified congenital malformationsQ89.81Kabuki syndromeQ89.89Other specified congenital malformationsQ89.9Congenital malformation, unspecified