ICD-10-CM > Q00-QA0 > Q80-Q89 > Q89 > Q89.0 Q89.0 Congenital absence and malformations of spleen Non-Billable/Non-Specific Type 1 Excludes isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6) Codes Q89.01Asplenia (congenital)Q89.09Congenital malformations of spleen