ICD-10-CM > Q00-QA0 > Q80-Q89 > Q89 > Q89.8 > Q89.81 Q89.81 Kabuki syndrome Billable/Specific Copy Code Copy Description Applicable To Kabuki syndrome, type 1, due to KMT2D mutationKabuki syndrome, type 2, due to KDM6A mutationNiikawa-Kuroki syndrome