ICD-10-CM > E00-E89 > E70-E88 > E74 > E74.1 E74.1 Disorders of fructose metabolism Non-Billable/Non-Specific Type 1 Excludes muscle phosphofructokinase deficiency (E74.09) Codes E74.10Disorder of fructose metabolism, unspecifiedE74.11Essential fructosuriaE74.12Hereditary fructose intoleranceE74.19Other disorders of fructose metabolism