ICD-10-CM > E00-E89 > E70-E88 > E71 > E71.1 > E71.11 E71.11 Branched-chain organic acidurias Non-Billable/Non-Specific Codes E71.110Isovaleric acidemiaE71.1113-methylglutaconic aciduriaE71.118Other branched-chain organic acidurias