ICD-10-CM > E00-E89 > E70-E88 > E71 > E71.1 E71.1 Other disorders of branched-chain amino-acid metabolism Non-Billable/Non-Specific Codes E71.11Branched-chain organic aciduriasE71.110Isovaleric acidemiaE71.1113-methylglutaconic aciduriaE71.118Other branched-chain organic aciduriasE71.12Disorders of propionate metabolismE71.120Methylmalonic acidemiaE71.121Propionic acidemiaE71.128Other disorders of propionate metabolismE71.19Other disorders of branched-chain amino-acid metabolism