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D89 Other disorders involving the immune mechanism, not elsewhere classified

Non-Billable/Non-Specific

Type 1 Excludes

  • hyperglobulinemia NOS (R77.1)
  • monoclonal gammopathy (of undetermined significance) (D47.2)

Type 2 Excludes

  • transplant failure and rejection (T86.-)

Codes

  • D89.0Polyclonal hypergammaglobulinemia
  • D89.1Cryoglobulinemia
  • D89.2Hypergammaglobulinemia, unspecified
  • D89.3Immune reconstitution syndrome
  • D89.4Mast cell activation syndrome and related disorders
    • D89.40Mast cell activation, unspecified
    • D89.41Monoclonal mast cell activation syndrome
    • D89.42Idiopathic mast cell activation syndrome
    • D89.43Secondary mast cell activation
    • D89.44Hereditary alpha tryptasemia
    • D89.49Other mast cell activation disorder
  • D89.8Other specified disorders involving the immune mechanism, not elsewhere classified
    • D89.81Graft-versus-host disease
      • D89.810Acute graft-versus-host disease
      • D89.811Chronic graft-versus-host disease
      • D89.812Acute on chronic graft-versus-host disease
      • D89.813Graft-versus-host disease, unspecified
    • D89.82Autoimmune lymphoproliferative syndrome [ALPS]
    • D89.83Cytokine release syndrome
      • D89.831Cytokine release syndrome, grade 1
      • D89.832Cytokine release syndrome, grade 2
      • D89.833Cytokine release syndrome, grade 3
      • D89.834Cytokine release syndrome, grade 4
      • D89.835Cytokine release syndrome, grade 5
      • D89.839Cytokine release syndrome, grade unspecified
    • D89.84IgG4-related disease
    • D89.89Other specified disorders involving the immune mechanism, not elsewhere classified
  • D89.9Disorder involving the immune mechanism, unspecified