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D89.4 Mast cell activation syndrome and related disorders

Non-Billable/Non-Specific

Type 1 Excludes

  • aggressive systemic mastocytosis (C96.21)
  • congenital cutaneous mastocytosis (Q82.2)
  • (non-congenital) cutaneous mastocytosis (D47.01)
  • (indolent) systemic mastocytosis (D47.02)
  • malignant mast cell neoplasm (C96.2-)
  • malignant mastocytoma (C96.29)
  • mast cell leukemia (C94.3-)
  • mast cell sarcoma (C96.22)
  • mastocytoma NOS (D47.09)
  • other mast cell neoplasms of uncertain behavior (D47.09)
  • systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)

Codes

  • D89.40Mast cell activation, unspecified
  • D89.41Monoclonal mast cell activation syndrome
  • D89.42Idiopathic mast cell activation syndrome
  • D89.43Secondary mast cell activation
  • D89.44Hereditary alpha tryptasemia
  • D89.49Other mast cell activation disorder