ICD-10-CM > E00-E89 > E70-E88 > E72 > E72.3 E72.3 Disorders of lysine and hydroxylysine metabolism Billable/Specific Copy Code Copy Description Applicable To Glutaric aciduria NOSGlutaric aciduria (type I)HydroxylysinemiaHyperlysinemia Type 1 Excludes glutaric aciduria type II (E71.313)Refsum's disease (G60.1)Zellweger syndrome (E71.510)