ICD-10-CM > E00-E89 > E70-E88 > E71 > E71.4 E71.4 Disorders of carnitine metabolism Non-Billable/Non-Specific Type 1 Excludes Muscle carnitine palmitoyltransferase deficiency (E71.314) Codes E71.40Disorder of carnitine metabolism, unspecifiedE71.41Primary carnitine deficiencyE71.42Carnitine deficiency due to inborn errors of metabolismE71.43Iatrogenic carnitine deficiencyE71.44Other secondary carnitine deficiencyE71.440Ruvalcaba-Myhre-Smith syndromeE71.448Other secondary carnitine deficiency