ICD-10-CM > D50-D89 > D80-D89 > D81 > D81.8 > D81.81 D81.81 Biotin-dependent carboxylase deficiency Non-Billable/Non-Specific Applicable To Multiple carboxylase deficiency Type 1 Excludes biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8) Codes D81.810Biotinidase deficiencyD81.818Other biotin-dependent carboxylase deficiencyD81.819Biotin-dependent carboxylase deficiency, unspecified