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D81.81 Biotin-dependent carboxylase deficiency

Non-Billable/Non-Specific

Applicable To

  • Multiple carboxylase deficiency

Type 1 Excludes

  • biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

Codes

  • D81.810Biotinidase deficiency
  • D81.818Other biotin-dependent carboxylase deficiency
  • D81.819Biotin-dependent carboxylase deficiency, unspecified