ICD-10-CM > D50-D89 > D80-D89 > D81 > D81.8 D81.8 Other combined immunodeficiencies Non-Billable/Non-Specific Codes D81.81Biotin-dependent carboxylase deficiencyD81.810Biotinidase deficiencyD81.818Other biotin-dependent carboxylase deficiencyD81.819Biotin-dependent carboxylase deficiency, unspecifiedD81.82Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]D81.89Other combined immunodeficiencies