ICD-10-CM > Q00-QA0 > Q80-Q89 > Q85 Q85 Phakomatoses, not elsewhere classified Non-Billable/Non-Specific Type 1 Excludes ataxia telangiectasia [Louis-Bar] (G11.3)familial dysautonomia [Riley-Day] (G90.1) Codes Q85.0Neurofibromatosis (nonmalignant)Q85.00Neurofibromatosis, unspecifiedQ85.01Neurofibromatosis, type 1Q85.02Neurofibromatosis, type 2Q85.03SchwannomatosisQ85.09Other neurofibromatosisQ85.1Tuberous sclerosisQ85.8Other phakomatoses, not elsewhere classifiedQ85.81PTEN hamartoma tumor syndromeQ85.82Other Cowden syndromeQ85.83Von Hippel-Lindau syndromeQ85.89Other phakomatoses, not elsewhere classifiedQ85.9Phakomatosis, unspecified