ICD-10-CM > Q00-QA0 > Q38-Q45 > Q38 > Q38.0 Q38.0 Congenital malformations of lips, not elsewhere classified Billable/Specific Copy Code Copy Description Applicable To Congenital fistula of lipCongenital malformation of lip NOSVan der Woude's syndrome Type 1 Excludes cleft lip (Q36.-)cleft lip with cleft palate (Q37.-)macrocheilia (Q18.6)microcheilia (Q18.7)