ICD-10-CM > Q00-QA0 > Q00-Q07 > Q07 > Q07.0 Q07.0 Arnold-Chiari syndrome Non-Billable/Non-Specific Applicable To Arnold-Chiari syndrome, type II Type 1 Excludes Arnold-Chiari syndrome, type III (Q01.-)Arnold-Chiari syndrome, type IV (Q04.8) Codes Q07.00Arnold-Chiari syndrome without spina bifida or hydrocephalusQ07.01Arnold-Chiari syndrome with spina bifidaQ07.02Arnold-Chiari syndrome with hydrocephalusQ07.03Arnold-Chiari syndrome with spina bifida and hydrocephalus