M04.8 Other autoinflammatory syndromes

Applicable To

• Blau syndrome
• Deficiency of interleukin 1 receptor antagonist [DIRA]
• Majeed syndrome
• Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
• Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]