ICD-10-CM > I00-I99 > I26-I28 > I27 > I27.8 > I27.83 I27.83 Eisenmenger's syndrome Billable/Specific Copy Code Copy Description Applicable To Eisenmenger's complex(Irreversible) Eisenmenger's diseasePulmonary hypertension with right to left shunt related to congenital heart disease Code Also underlying heart defect, if known, such as:atrial septal defect (Q21.1-)Eisenmenger's defect (Q21.8)patent ductus arteriosus (Q25.0)ventricular septal defect (Q21.0)