ICD-10-CM > I00-I99 > I26-I28 > I27 > I27.0 I27.0 Primary pulmonary hypertension Billable/Specific Copy Code Copy Description Applicable To Heritable pulmonary arterial hypertensionIdiopathic pulmonary arterial hypertensionPrimary group 1 pulmonary hypertensionPrimary pulmonary arterial hypertension Type 1 Excludes persistent pulmonary hypertension of newborn (P29.30)pulmonary hypertension NOS (I27.20)secondary pulmonary arterial hypertension (I27.21)secondary pulmonary hypertension (I27.29)