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I27.0 Primary pulmonary hypertension

Billable/Specific

Applicable To

  • Heritable pulmonary arterial hypertension
  • Idiopathic pulmonary arterial hypertension
  • Primary group 1 pulmonary hypertension
  • Primary pulmonary arterial hypertension

Type 1 Excludes

  • persistent pulmonary hypertension of newborn (P29.30)
  • pulmonary hypertension NOS (I27.20)
  • secondary pulmonary arterial hypertension (I27.21)
  • secondary pulmonary hypertension (I27.29)