ICD-10-CM > C00-D49 > C81-C96 > C88 > C88.0 C88.0 Waldenström macroglobulinemia Non-Billable/Non-Specific Applicable To Lymphoplasmacytic lymphoma with IgM-productionMacroglobulinemia (idiopathic) (primary) Type 1 Excludes small cell B-cell lymphoma (C83.0) Codes C88.00Waldenström macroglobulinemia not having achieved remissionC88.01Waldenström macroglobulinemia, in remission