ICD-10-CM > A00-B99 > A80-A89 > A81 > A81.0 A81.0 Creutzfeldt-Jakob disease Non-Billable/Non-Specific Codes A81.00Creutzfeldt-Jakob disease, unspecifiedA81.01Variant Creutzfeldt-Jakob diseaseA81.09Other Creutzfeldt-Jakob disease