ICD-10-CM>Q00-QA1>Q90-Q99>Q99>Q99.8>Q99.81Q99.81Usher syndromeNon-Billable/Non-SpecificUse Additionalcode to identify any auditory and visual manifestationsCodesQ99.811Usher syndrome, type 1Q99.812Usher syndrome, type 2Q99.813Usher syndrome, type 3Q99.818Other Usher syndromeQ99.819Usher syndrome, unspecified