ICD-10-CM>Q00-QA1>Q80-Q89>Q89>Q89.8>Q89.81Q89.81Kabuki syndromeBillable/Specific Copy Code Copy DescriptionApplicable ToKabuki syndrome, type 1, due to KMT2D mutationKabuki syndrome, type 2, due to KDM6A mutationNiikawa-Kuroki syndrome