ICD-10-CM>Q00-QA1>Q80-Q89>Q87>Q87.AQ87.ALoeys-Dietz syndromeBillable/Specific Copy Code Copy DescriptionType 1 Excludesarterial tortuosity syndrome (Q87.82)Ehlers-Danlos syndrome (Q79.6)Marfan syndrome (Q87.40-Q87.43)other systemic involvement of connective tissue (M35)