ICD-10-CM>Q00-QA1>Q80-Q89>Q85Q85Phakomatoses, not elsewhere classifiedNon-Billable/Non-SpecificType 1 Excludesataxia telangiectasia [Louis-Bar] (G11.3)familial dysautonomia [Riley-Day] (G90.1)CodesQ85.0Neurofibromatosis (nonmalignant)Q85.00Neurofibromatosis, unspecifiedQ85.01Neurofibromatosis, type 1Q85.02Neurofibromatosis, type 2Q85.03SchwannomatosisQ85.09Other neurofibromatosisQ85.1Tuberous sclerosisQ85.8Other phakomatoses, not elsewhere classifiedQ85.81PTEN hamartoma tumor syndromeQ85.82Other Cowden syndromeQ85.83Von Hippel-Lindau syndromeQ85.89Other phakomatoses, not elsewhere classifiedQ85.9Phakomatosis, unspecified