ICD-10-CM>Q00-QA1>Q00-Q07>Q07>Q07.0Q07.0Arnold-Chiari syndromeNon-Billable/Non-SpecificApplicable ToArnold-Chiari syndrome, type IIType 1 ExcludesArnold-Chiari syndrome, type III (Q01.-)Arnold-Chiari syndrome, type IV (Q04.8)CodesQ07.00Arnold-Chiari syndrome without spina bifida or hydrocephalusQ07.01Arnold-Chiari syndrome with spina bifidaQ07.02Arnold-Chiari syndrome with hydrocephalusQ07.03Arnold-Chiari syndrome with spina bifida and hydrocephalus